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CASE REPORT
Year : 2021  |  Volume : 6  |  Issue : 1  |  Page : 28-30

Orofacial manifestations in a child with congenital lamellar ichthyosis: Practical recommendations for dental management


Department of Pedodontics and Preventive Dentistry, University College of Medical Sciences, Guru Teg Bahadur Hospital, New Delhi, India

Correspondence Address:
Puja Sabherwal
Department of Pedodontics and Preventive Dentistry, University College of Medical Sciences, Guru Teg Bahadur Hospital, New Delhi
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/ijpr.ijpr_17_20

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Ichthyosis is a group of rare Mendelian disorders which affects cornification of the skin characterized by hyperkeratosis and/or scaling. The incidence of lamellar ichthyosis is estimated to be approximately 1 in 300,000 live births with no known sex predilection. The presenting features comprise a wide array of dermatological manifestations. This case illustrates findings in a 5-year-old child with the rare disorder, i.e., congenital lamellar ichthyosis with a history of rickets with interesting array of orofacial manifestations associated with the disease. The dental management may include a multispecialty approach for rehabilitation while using delicate approach to manipulate soft tissues and skin. We share a few practical recommendations which were helpful for allaying challenges we faced in this case.


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